• Olvis Petre Pulmonology Department, “Shefqet Ndroqi” University Hospital, Albania https://orcid.org/0000-0002-0646-0484
  • Tashi Bani Irma Pulmonology Department, “Shefqet Ndroqi” University Hospital, Albania
  • Hasani Jola Pulmonology Department, “Shefqet Ndroqi” University Hospital, Albania
  • Shestani Justi Pulmonology Department, “Shefqet Ndroqi” University Hospital, Albania
  • Bala Silvana Pulmonology Department, “Shefqet Ndroqi” University Hospital, Albania
  • Hafizi Hasan Pulmonology Department, “Shefqet Ndroqi” University Hospital, Albania




Unilateral Pulmonary Artery Atresia/Agenesis, Pulmonary Hypertension, Isolated Pulmonary Artery Agenesis.

Abstract [English]

A twenty-three-year-old male truck driver with a 12-pack year smoking history and no previous history of hospitalization was admitted to the “Shefqet Ndroqi” University Hospital pulmonology department after a cardiologist consultation where he was diagnosed with pulmonary hypertension. Two of the patient’s uncles from his mother’s side died during their pediatric age from congenital heart defects. A contrast-enhanced chest computed tomography was performed, and it showed an interruption of the lumen of the proximal part of the left pulmonary artery (atresia), a reduction of the left lung parenchyma volume, and bilateral pulmonary emphysema. The respiratory functional tests detected a moderate obstructive syndrome, and the 6MWT detected a decrease in arterial partial pressure of oxygen and oxygen saturation level. A diagnosis of unilateral pulmonary artery atresia/agenesis was confirmed.


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How to Cite

Petre, O., Irma, T. B., Jola, H., Justi, S., Silvana, B., & Hasan, H. (2022). UNILATERAL PULMONARY ARTERY ATRESIA/AGENESIS: A CASE REPORT. International Journal of Research -GRANTHAALAYAH, 10(12), 13–17. https://doi.org/10.29121/granthaalayah.v10.i12.2022.4930

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